Fig. 8.1 Schematic representation of the clinical spectrum of retroperitoneal fibrosis and chronic periaortitis 8.2 Secondary Forms of RPF The clinical entities included in the spectrum of CP are idiopathic….
Fig. 2.1 Myofibroblasts are central to fibrogenesis and are submitted to regulation by pro- and anti-fibrotic cytokines. Schematic and simplified view of the network of cytokines influencing ECM deposition by…
Gene/locus and variation/allele Population Cases Controls Odds ratio P-Value Reference HLA-B (rs3099844) Norwegian 285 PSC 298 4.8 2.6 × 10−26 Karlsen et al. [19] GPC6 (rs9524260) Norwegian 285 PSC 298…
Fig. 6.1 (a) Computed tomography (CT) appearance of diffuse AIP: the pancreatic parenchyma appears diffusely hypodense in the body-tail of the pancreas on arterial phase. (b) CT appearance of focal…
© Springer International Publishing Switzerland 2017Augusto Vaglio (ed.)Systemic Fibroinflammatory DisordersRare Diseases of the Immune System10.1007/978-3-319-41349-5_5 5. Pathophysiology of IgG4-Related Disease Jochen Zwerina1 (1) Ludwig Boltzmann Institute of Osteology at the Hanusch Hospital of WGKK and…
