Growing Up with Liver Disease
Barrier to adherence Strategies Naive about the risks of non-adherence Individualized education about illness and medication Burden of medication regime: too many tablets or too many times a day Simplify…
Pediatric Liver Transplantation
© Springer International Publishing Switzerland 2016Stefano Guandalini, Anil Dhawan and David Branski (eds.)Textbook of Pediatric Gastroenterology, Hepatology and Nutrition10.1007/978-3-319-17169-2_73 73. Pediatric Liver Transplantation Nigel Heaton1 (1) King’s Health Partners, Institute of Liver Studies, Kings College Hospital FT…
Nutritional Management of Children with Liver Disease
Causes of malnutrition Contributing factors Decreased nutrient intake Nausea and vomiting Pruritis Taste changes Unpalatable diets/specialist feeds Reduced gastric capacity and discomfort from ascites or organomegaly Fluid and sodium restriction…
Celiac Disease
Fig. 40.1 CD pathogenesis. Celiac disease ( CD) is a multifactorial disorder induced by gluten in genetically susceptible subjects. Several environmental factors (i.e., viral infections, alterations in microbiome composition, etc.)…
Disorders of Sucking and Swallowing
(1) Section of Pediatrics, Department of Transitional Medical Science, University of Naples “Federico II”, Via S. Pansini 5, 80131 Naples, Italy Francesca Paola Giugliano Email: staiano@unina.it KeywordsDysphagiaSwallowingSuckingNeurological disordersMalnutritionVideofluoroscopy Introduction The…
Congenital Disorders of Lipid Transport
Fig. 38.1 Overview of intestinal lipid absorption: Key genetic regulators. Following digestion of dietary and biliary lipid, the component lipid species including long-chain fatty acid (FA), monoglycerides (MG), and cholesterol…
Liver Disease in Primary Immunodeficiencies
Fig. 62.1 Endoscopic retrograde cholangio-pancreatogram showing diffuse bilateral intra- and extrahepatic cholangiopathy in a child with a form of hyper IgE syndrome (DOCK8 deficiency) ERCP demonstrating diffuse CS-positive cholangiopathy in…
Bacterial, Fungal and Parasitic Infections of the Liver
© Springer International Publishing Switzerland 2016Stefano Guandalini, Anil Dhawan and David Branski (eds.)Textbook of Pediatric Gastroenterology, Hepatology and Nutrition10.1007/978-3-319-17169-2_61 61. Bacterial, Fungal and Parasitic Infections of the Liver Anita Verma1 (1) Institute of Liver Studies, King’s College…
Chronic Viral Hepatitis B and C
Fig. 60.1 Illustration of the different phases of chronic hepatitis B. HBV-DNA hepatitis B virus deoxyribonucleic acid, DNA-PCR deoxyribonucleic acid polymerase chain reaction, HBV hepatitis B virus, HBsAg hepatitis B…
Chronic Intestinal Pseudo-Obstruction in Childhood
Primary CIPO Sporadic or familial forms of hollow visceral myopathy/neuropathy (e.g., megacystis microcolon intestinal hypoperistalsis syndrome) [7, 27–44] Mitochondrial neurogastrointestinal encephalomyopathy (MNGIE) [18, 45–47] Hirschsprung’s disease [48–50] Neuropathy associated with…
